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KMID : 0361020150580100729
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Korean Journal of Otolaryngology - Head and Neck Surgery
2015 Volume.58 No. 10 p.729 ~ p.733
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Hemangioma of Endolymphatic Sac in Von Hippel-Lindau Patient
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이여진:Yi Yeo-Jeen
김예원:Kim Ye-Won/박성혜:Park Sung-Hye/박무균:Park Moo-Kyun
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Abstract
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The present study reports a rare case of capillary hemangioma of endolymphatic sac. A 23-year-old male who underwent von Hippel-Lindau disease presented with recurrent sudden sensorineural hearing loss. Magnetic resonance imaging revealed a heterogenous enhanced mass in the right endolymphatic sac, which was hyperintense on the enhanced T1-weighted images and inhomogenous on the T2-weighted images. Pre-operatively, this tumor was believed to be an endolymphatic sac tumor because of the history of von Hippel-Lindau disease. During the surgery, vascular tumor was removed by transmastoid approach. A histopathological examination indicated that the tumor was a capillary hemangioma. To the best of our knowledge, the present study is the second case of hemangioma in the endolymphatic sac and first case of von Hippel-Lindau disease.
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KEYWORD
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Endolymphatic sac tumor, Hemangioma, Sudden sensorineural hearing loss, Von Hippel-Lindau disease
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